Hipoplasia pulmonar: análisis de la casuística durante 20 años

Yanny Paola Delgado-Peña*, Alba Torrent-Vernetta, Gabriela Sacoto, Inés de Mir-Messa, Sandra Rovira-Amigo, Silvia Gartner, Antonio Moreno-Galdó, José Andrés Molino-Gahete, Felíx Castillo-Salinas

*Autor correspondiente de este trabajo

Producción científica: Contribución a una revistaArtículoInvestigaciónrevisión exhaustiva

10 Citas (Scopus)

Resumen

Introduction Pulmonary hypoplasia is the most frequent congenital anomaly associated with perinatal mortality. Material and methods A retrospective and descriptive review was conducted on cases of patients diagnosed with pulmonary hypoplasia between 1995 and 2014 in a tertiary university hospital. An analysis was made of the prenatal imaging, clinical manifestations, post-natal diagnostic tests, treatment and management, long-term follow up, and survival data. Results A total of 60 cases were identified, all of them with prenatal imaging. Sixteen patients required foetal surgery. Congenital diaphragmatic hernia was the most frequent diagnosis. Main clinical presentation was respiratory distress with severe hypoxemia and high requirements of mechanical ventilation. Mortality rate was 47% within first 60 days of life, and 75% for the first day of life. Pneumonia and recurrent bronchitis episodes were observed during follow-up. They had a lung function obstructive pattern, and their quality of life and exercise tolerance was good. Conclusions High neonatal mortality and significant long-term morbidity associated with pulmonary hypoplasia requires an early diagnosis and a specialised multidisciplinary team management.
Título traducido de la contribuciónPulmonary hypoplasia: An analysis of cases over a 20-year period
Idioma originalEspañol
Páginas (desde-hasta)70-76
Número de páginas7
PublicaciónAnales de Pediatria
Volumen85
N.º2
DOI
EstadoPublicada - 1 ago 2016

Palabras clave

  • Congenital diaphragmatic hernia
  • Lung hypoplasia
  • Pulmonary agenesis
  • Pulmonary hypoplasia

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