Curative partial hepatectomy in adult Caroli's disease

Rodrigo Medrano-Caviedes, Vicente Artigas, Francisco J. Sancho, Guillermo Marín-Hargreaves, Manuel Rodríguez, Manuel Trías

    Research output: Contribution to journalArticleResearchpeer-review

    6 Citations (Scopus)

    Abstract

    Caroli's disease consists of a congenital malformation of the intrahepatic bile ducts characterized by saccular, segmental, cystic dilatations giving rise to recurrent cholangitis. The inheritance pattern is unclear and the disease may be associated with other hereditary diseases such as adult polycystic kidney disease. The most effective therapeutic option in symptomatic unilobar Caroli's disease is resection of the affected lobe. In bilobar involvement, liver transplantation should be considered. Due to their rarity, we report three cases of Caroli's disease successfully resolved through lobectomy of the affected lobe: two patients with recurrent cholangitis and one patient with associated adult polycystic kidney disease.
    Original languageEnglish
    Pages (from-to)218-221
    JournalCirugia Espanola
    Volume81
    Issue number4
    DOIs
    Publication statusPublished - 1 Jan 2007

    Keywords

    • Adult polycystic kidney disease
    • Caroli's disease
    • Cholangitis
    • Liver resection

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