Curative partial hepatectomy in adult Caroli's disease

Rodrigo Medrano-Caviedes; Vicente Artigas; Francisco J. Sancho; Guillermo Marín-Hargreaves; Manuel Rodríguez; Manuel Trías

doi:10.1016/S0009-739X(07)71303-9

Curative partial hepatectomy in adult Caroli's disease

Rodrigo Medrano-Caviedes, Vicente Artigas, Francisco J. Sancho, Guillermo Marín-Hargreaves, Manuel Rodríguez, Manuel Trías

Research output: Contribution to journal › Article › Research › peer-review

6 Citations (Scopus)

Abstract

Caroli's disease consists of a congenital malformation of the intrahepatic bile ducts characterized by saccular, segmental, cystic dilatations giving rise to recurrent cholangitis. The inheritance pattern is unclear and the disease may be associated with other hereditary diseases such as adult polycystic kidney disease. The most effective therapeutic option in symptomatic unilobar Caroli's disease is resection of the affected lobe. In bilobar involvement, liver transplantation should be considered. Due to their rarity, we report three cases of Caroli's disease successfully resolved through lobectomy of the affected lobe: two patients with recurrent cholangitis and one patient with associated adult polycystic kidney disease.

Original language	English
Pages (from-to)	218-221
Journal	Cirugia Espanola
Volume	81
Issue number	4
DOIs	https://doi.org/10.1016/S0009-739X(07)71303-9
Publication status	Published - 1 Jan 2007

Keywords

Adult polycystic kidney disease
Caroli's disease
Cholangitis
Liver resection

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10.1016/S0009-739X(07)71303-9

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title = "Curative partial hepatectomy in adult Caroli's disease",

abstract = "Caroli's disease consists of a congenital malformation of the intrahepatic bile ducts characterized by saccular, segmental, cystic dilatations giving rise to recurrent cholangitis. The inheritance pattern is unclear and the disease may be associated with other hereditary diseases such as adult polycystic kidney disease. The most effective therapeutic option in symptomatic unilobar Caroli's disease is resection of the affected lobe. In bilobar involvement, liver transplantation should be considered. Due to their rarity, we report three cases of Caroli's disease successfully resolved through lobectomy of the affected lobe: two patients with recurrent cholangitis and one patient with associated adult polycystic kidney disease.",

keywords = "Adult polycystic kidney disease, Caroli's disease, Cholangitis, Liver resection",

author = "Rodrigo Medrano-Caviedes and Vicente Artigas and Sancho, {Francisco J.} and Guillermo Mar{\'i}n-Hargreaves and Manuel Rodr{\'i}guez and Manuel Tr{\'i}as",

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T1 - Curative partial hepatectomy in adult Caroli's disease

AU - Medrano-Caviedes, Rodrigo

AU - Artigas, Vicente

AU - Sancho, Francisco J.

AU - Marín-Hargreaves, Guillermo

AU - Rodríguez, Manuel

AU - Trías, Manuel

PY - 2007/1/1

Y1 - 2007/1/1

N2 - Caroli's disease consists of a congenital malformation of the intrahepatic bile ducts characterized by saccular, segmental, cystic dilatations giving rise to recurrent cholangitis. The inheritance pattern is unclear and the disease may be associated with other hereditary diseases such as adult polycystic kidney disease. The most effective therapeutic option in symptomatic unilobar Caroli's disease is resection of the affected lobe. In bilobar involvement, liver transplantation should be considered. Due to their rarity, we report three cases of Caroli's disease successfully resolved through lobectomy of the affected lobe: two patients with recurrent cholangitis and one patient with associated adult polycystic kidney disease.

AB - Caroli's disease consists of a congenital malformation of the intrahepatic bile ducts characterized by saccular, segmental, cystic dilatations giving rise to recurrent cholangitis. The inheritance pattern is unclear and the disease may be associated with other hereditary diseases such as adult polycystic kidney disease. The most effective therapeutic option in symptomatic unilobar Caroli's disease is resection of the affected lobe. In bilobar involvement, liver transplantation should be considered. Due to their rarity, we report three cases of Caroli's disease successfully resolved through lobectomy of the affected lobe: two patients with recurrent cholangitis and one patient with associated adult polycystic kidney disease.

KW - Adult polycystic kidney disease

KW - Caroli's disease

KW - Cholangitis

KW - Liver resection

U2 - 10.1016/S0009-739X(07)71303-9

DO - 10.1016/S0009-739X(07)71303-9

M3 - Article

VL - 81

SP - 218

EP - 221

IS - 4

ER -

Curative partial hepatectomy in adult Caroli's disease

Abstract

Keywords

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